Non-invasive respiratory approach in a child diagnosed with spinal muscular atrophy type II and massive atelectasis: a case report
Abstract
Introduction: There is evidence supporting the benefits of non-invasive treatment for acute respiratory failure (ARF) associated with spinal muscular atrophy (SMA). However, to date, no case reports describing the non-invasive management of ARF due to massive atelectasis in patients with SMA are available in our country. The aim of this study is to describe the non-invasive respiratory approach in a child with SMA type II who was admitted with ARF and massive atelectasis to a public pediatric hospital.
Case presentation: A 10-year-old child diagnosed with SMA type II was admitted with respiratory failure due to massive atelectasis of the left lung. Non-invasive measures were implemented, including proper positioning, enhanced use of airway clearance techniques, prolonged non-invasive ventilation, optimization of ventilatory support equipment, and interface. After five days of treatment, a significant improvement in atelectasis was observed. On the eighth day, the patient was discharged.
Conclusion: We described the non-invasive respiratory approach in a child with SMA type II, which proved to be beneficial in addressing ARF and massive atelectasis.
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