Use of a mechanical insufflation-exsufflation device at home in pediatric subjects with neuromuscular disease
Case series
Abstract
Objective: To describe the use of a mechanical insufflation-exsufflation (MIE) device at home in followed-up pediatric subjects with neuromuscular disease after discharge from a pediatric hospital, in the Autonomous City of Buenos Aires.
Materials and method: An observational, descriptive, cross-sectional, retrospective study was conducted. We included in the study all pediatric neuromuscular subjects who had been using an MIE device at home for >6 months between January 2018 and April 2019.
Results: A total of 59 subjects were analyzed, with a mean age of 8.84 (SD 4.01) years. The most common diagnosis was spinal muscular atrophy (SMA) type II, which was present in 32 (54.2%) cases. The subjects began using the MIE device at a mean age of 4 (IQR 3-7) years, and it was prescribed mainly due to recurrent respiratory tract infections. Most subjects used the Philips Respironics E70® device —positive and negative pressures of 40 cm H2O, in automatic mode— and an oronasal mask interface. No complications were reported.
Conclusion: The most prevalent diagnosis for pediatric subjects who used an MIE device was SMA. The devices were mainly prescribed due to recurrent respiratory tract infections and mostly operated by parents, in automatic mode, with positive and negative pressures of 40 cm H2O.
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